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DeCS
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Descriptor English:
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Hemoglobinuria, Paroxysmal
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Descriptor Spanish:
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Hemoglobinuria Paroxística
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Descriptor Portuguese:
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Hemoglobinúria Paroxística
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Synonyms English:
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Cold Paroxysmal Hemoglobinuria
Hemoglobinuria, Cold Paroxysmal
Hemoglobinuria, Nocturnal Paroxysmal
Hemoglobinuria, Paroxysmal Cold
Hemoglobinuria, Paroxysmal Nocturnal
Marchiafava Micheli Syndrome
Marchiafava-Micheli Syndrome
Nocturnal Paroxysmal Hemoglobinuria
Paroxysmal Cold Hemoglobinuria
Paroxysmal Hemoglobinuria
Paroxysmal Hemoglobinuria, Cold
Paroxysmal Hemoglobinuria, Nocturnal
Paroxysmal Nocturnal Hemoglobinuria
Syndrome, Marchiafava-Micheli
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Tree Number:
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C15.378.071.141.560
C15.378.190.625.460
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Definition English:
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A condition characterized by the recurrence of HEMOGLOBINURIA caused by intravascular HEMOLYSIS. In cases occurring upon cold exposure (paroxysmal cold hemoglobinuria), usually after infections, there is a circulating antibody which is also a cold hemolysin. In cases occurring during or after sleep (paroxysmal nocturnal hemoglobinuria), the clonal hematopoietic stem cells exhibit a global deficiency of cell membrane proteins. |
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History Note English:
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78; was MARCHIAFAVA-MICHELI SYNDROME 1963-77
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Allowable Qualifiers English:
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Record Number:
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6607
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Unique Identifier:
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D006457
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Occurrence in VHL:
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Similar:
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DeCS
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